From: Neurological phenotypes in patients with NLRP3-, MEFV-, and TNFRSF1A low-penetrance variants
All | NLRP3 variants w/o MS | NLRP3 variants with MS | MEFV variants w/o MS | MEFV variants with MS | TNFRSF1A variants w/o MS | TNFRSF1A variants with MS | |
---|---|---|---|---|---|---|---|
CRP (mg/dl) | 2.7 ± 1.6 (54) (0.6-86) | 2.2 ± 2.0 (7) (0.6-10.1) | 2.1 ± 1.2 (3) (0.8-2.8) | 4.7 ± 8.9 (10) (0.65-86) | 1.7 ± 1.5 (16) (0.6-11.5) | 0.7 ± 0.1 (2) (0.7-0.8) | 4.7 ± 6.6 (16) (0.6-23.8) |
Leucocytes (G/l) | 13.3 ± 0.6 (36) (10.5–31.9) | 13.5 ± 2.4 (6) (10.3–29) | 14.1 ± 3.1 (4) (10.7–31.9) | 13.2 ± 1.5 (7) (11.1–19.3) | 12.5 ± 2.1 (8) (10.5–16.6) | - | 13.0 ± 2.1 (11) (11.3-18.6) |
SAA (mg/dl) | 31 ± 36.2 (68) (5.2-3115) | 172.2 ± 492.9 (11) (5.2-3115) | 21.7 ± 32.8 (8) (5.2-107) | 10.5 ± 5.1 (9) (6.0-22.1) | 95 ± 298.2 (14) (5.2-1130) | 9.4 ± 3.0 (5) (5.7-13-1) | 18.4 ± 25 (21) (5.2-122) |